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纳尔逊综合征
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纳尔逊综合征
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Nelson syndrome
纳尔逊综合征
库欣病[注](垂体性皮质醇增多症)患者行双侧肾上腺切除后,由于缺乏皮质醇对下丘脑促肾上腺皮质激素释放激素(CRH)的负反馈抑制作用,导致CRH分泌过多,长期刺激原来存在的垂体ACTH瘤,出现的进行性皮肤黏膜色素沉着、闭经、视力障碍、视野障碍、高ACTH分泌的垂体瘤伴蝶鞍扩大等一系列临床综合征。
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