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无神经节细胞症
释义
无神经节细胞症
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医学
外科学
释
aganglionosis
无神经节细胞症
病变肠壁神经丛异常和神经节细胞缺如、减少或发育不良,致使肠管持续痉挛不能正常蠕动而引起的以排便功能障碍为主的疾病。又称先天性巨结肠(congenital megacolon)。消化道最常见的先天性畸形之一。
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