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tuberous sclerosis
释义
tuberous sclerosis
Encyclopedia
医学
结节性硬化
释
tuberous sclerosis
结节性硬化
由源于外胚层的器官发育异常所致,病变累及神经系统、皮肤和眼,也可累及中胚层、内胚层器官和心、肺、骨、肾和胃肠等。临床以面部皮脂腺瘤、癫痫发作及智能减退为特征。
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