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hyper-IgE syndrome
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hyper-IgE syndrome
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血液系统
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hyper-IgE syndrome
高免疫球蛋白E综合征
一种以皮肤、肺、关节和内脏反复葡萄球菌感染,嗜酸性粒细胞增多及血清免疫球蛋白E(IgE)浓度显著增高为特征的遗传性免疫缺陷综合征。简称HIES。又称约伯综合征。
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