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Fabry disease
释义
Fabry disease
Encyclopedia
医学
法布里病
释
Fabry disease
法布里病
X染色体连锁隐性遗传的先天性糖鞘磷脂代谢异常的疾病。是由细胞溶酶体内α-半乳糖苷酶先天性活性降低或缺乏导致的代谢性疾病。又称α-半乳糖苷酶缺乏症。
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polarization extinction method
polarization fading
polarization fluorimeter
polarization function
polarization Green function
polarization Green's function
polarization identity
polarization illumination
polarization index
polarization infrared technique
polarization intensity vector
polarization interference filter
polarization interferometer
polarization interferometry
polarization labeling spectroscopy
polarization loss
polarization maintaining fiber
polarization-maintaining fiber
polarization measurement
polarization measuring device
polarization microscope
polarization modal dispersion
polarization modulation
polarization modulation measurement principle
polarization of an Abelian variety
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