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单词
Fabry disease
释义
Fabry disease
Encyclopedia
医学
法布里病
释
Fabry disease
法布里病
X染色体连锁隐性遗传的先天性糖鞘磷脂代谢异常的疾病。是由细胞溶酶体内α-半乳糖苷酶先天性活性降低或缺乏导致的代谢性疾病。又称α-半乳糖苷酶缺乏症。
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turbidimetry; turbidimetric method
turbidite
turbidity
turbidity analyzer
turbidity coefficient
turbidity current
turbidity sediment
turbidity sensor
turbid medium
turbidometer
turbid sperm
turbid urine
turbine
turbine adiabatic efficiency
turbine automatic start-up and shut-down control
turbine available isentropic expansion work
turbine based combined cycle engine
turbine based rocket and ramjet combined engine
turbine blade cooling effect
turbine blade profile
turbine cascade
Turbine characteristics
turbine characteristic Test
turbine compressor
turbine cooling system
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更新时间:2026/1/18 2:26:58